what is systemic sclerosis ?
what is systemic sclerosis？
Scleroderma (sklair-oh-DUR-muh), also known as systemic sclerosis, is a group of rare diseases that involve the hardening and tightening of the skin. It may also cause problems in the blood vessels, internal organs and digestive tract.2022年1月27日
Furthermore,Is systemic sclerosis serious?
Systemic sclerosis (SSc, scleroderma) is the most serious form of the disease. This form of scleroderma can occur at any age but is most common in women of childbearing age.
Beside above,How long can you live with systemic sclerosis?
Patients with limited cutaneous systemic sclerosis have a 10-year survival estimate of approximately 90%. However, development of interstitial lung disease (ILD) or pulmonary artery hypertension (PAH) dramatically increases the risk of death.
Considering this,What is meant by systemic sclerosis?
(sis-TEH-mik skleh-ROH-sis) A disease that is marked by hardening and thickening of skin, connective tissue that surrounds other tissues and organs, and blood vessels. Also called systemic scleroderma.
Also asked,Is systemic sclerosis curable?
There is no cure for systemic sclerosis. No drug can stop the progression of systemic sclerosis. However, drugs can relieve some symptoms and reduce organ damage.
What is the difference between scleroderma and systemic sclerosis?
What's the difference between scleroderma and systemic sclerosis? Scleroderma is seen only on the skin. However, when the fibrosis involves your other internal organs, this is considered systemic sclerosis.
How quickly does systemic sclerosis progress?
In our cohort, 56% of observed progression occurred within 5 years since the first non-Raynaud symptom. While progression in skin involvement occurred more frequently in early disease, the proportion of patients with lung, heart or GI progression was relatively stable over time.
What can I expect from systemic sclerosis?
Key Points. Key findings in systemic sclerosis include skin and joint changes, Raynaud phenomenon, and esophageal changes, but life-threatening effects may involve organs such as the lungs, heart, or kidneys.
Is systemic sclerosis a death sentence?
Systemic sclerosis (SSc) is a multisystem disease that is often fatal. Since 1980, the successful treatment of scleroderma renal crisis (SRC) has dramatically decreased mortality from SSc.
What were your first symptoms of scleroderma?
Early symptoms may include swelling and itchiness. Affected skin can become lighter or darker in color and may look shiny because of the tightness. Some people also experience small red spots, called telangiectasia, on their hands and face.
What is the life expectancy of a person with scleroderma?
People who have localized scleroderma may live an uninterrupted life with only minor symptom experiences and management. On the other hand, those diagnosed with an advanced and systemic version of the disease have a prognosis of anywhere from three to 15 years.
How do you test for systemic sclerosis?
Because systemic sclerosis (SSc) is a chronic illness, regular monitoring is needed to assess disease activity and progression. Laboratory tests for monitoring may include erythrocyte sedimentation rate (ESR) and/or C-reactive protein (CRP), CBC, liver function, creatinine, urea, and urinary protein tests.
What foods should be avoided with scleroderma?
REFLUX/HEARTBURN: eat small frequent meals to avoid overfilling your stomach; avoid eating within 2-3 hours of bedtime; avoid foods that may aggravate symptoms such as citrus fruits, tomato products, greasy fried foods, coffee, garlic, onions, peppermint, gas-producing foods (such as raw peppers, beans, broccoli, raw ...